Oral Surg Oral Med Oral Pathol. Dec;68(6) Familial gigantiform cementoma: classification and presentation of a large pedigree. Young SK(1). Gigantiform cementoma is a rare, benign fibro-cemento-osseous disease of the jaws, seen most frequently in young girls. Radiographically, it typically presents. PDF | Familial gigantiform cementoma is an exceedingly rare but distinct subtype of cemento-osseous-fibrous lesion. Undocumented.

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Besides, the informed consent was obtained from these patients. All these results came out with no marked aberrance.

Large vascular malformation in a child presenting with vascular steal phenomenon managed with pial synangiosis. Cemento-osseous dysplasia in Jamaica: Axial CT image showing the radiodense lobular mass surrounded by a radiolucent margin.


Familial gigantiform gigzntiform is an exceedingly rare but distinct subtype of cemento-osseous-fibrous lesion. All teeth vigantiform to the first primary molar were absent, owing to previous extractions, and the remaining tooth germs were displaced. Based on findings garnered from CT, it was noteworthy that 2 big circular deficits could be easily detected on both sides of the iliac bones.

However, extragnathic presentations of FGC in patients have often been neglected, owing in part to rarity of this disease. As a direct consequence, physical deterioration was also found by his parents. Radiographic examination revealed a well-circumscribed lobular radio-opaque mass surrounded by a radiolucent margin. Furthermore, radiographic examinations of calvaria, pelvis, femoris, tibia, cementoam fibula all revealed radiolucent areas signifying diffuse osteopenic bone losses.

Apart from typical multiquadrant and expansile abnormalies involving both jaws, he also givantiform from several times of fractures in lower extremity. Please review our privacy policy. Microscopic examination showed mineralized bone with obliterated marrow spaces containing inactive fibrous tissue Figure 5.


Despite the paucity of information regarding FGC, DEA, as we believe, carries diagnostic and therapeutic implications, along with other radiographic examinations. She is currently under treatment, which she may need to continue until her growth stops in her early 20s.

Gigantiform cementoma

A review and differential diagnosis. Macdonald Oral surgery, oral medicine, oral pathology and….

Arteriovenous malformation of the scalp with cerebral steal. This dentistry article is a stub. A provisional diagnosis of an osteoma was made and the lesion was enucleated through the buccal ecmentoma plate. The sharp contrast of CT images between densely bony deposits in FGC lesion and the radiolucent low-density images confirmed our hypothesis that both maxilla and mandible of FGC shared unevenly and favorable distribution of calcium deposits in the general calcium metabolism of whole body.

A clinical and radiologic spectrum of cases. Clinical features demonstrating expansion of the left maxilla by a firm mass. Please consider making a donation now and gigsntiform in the future. Furthermore, the medical history of the child was uneventful. National Center for Biotechnology InformationU.

Gigantiform cementoma – Wikipedia

Therefore, we present a case with a large FGC family history so as to sketch a more detailed portrait of such ailment. You can help Wikipedia by expanding it.

To keep both practitioners and patients informed of the overall bony changes and corresponding risks of fractures, we contended that DEA should be routinely tested since initial clinic visit. Microscopic examination showed a lobular calcified mass with giganntiform peripheral zone of fibropsammomatous tissue corresponding with the radiolucent margin.

Support Center Support Center. The disorder appears to occur mainly in asymptomatic black females with a mean age of onset of 42 years. Gardner’s Syndrome — the importance of early diagnosis: NarayanWilfried Wagner Oral surgery, oral medicine, oral pathology and….


Familial Gigantiform Cementoma

Pediatr Blood Cancer ; Florid osseous dysplasia, which is histologically similar, may be distinct. Obliteration of the maxillary sinus and expansion of the maxillary bony cortex was noted. Please help improve this article by adding citations to reliable sources.

The term has been used in the past to describe florid cemento-osseous dysplasiabut it is now reserved for an autosomal dominant condition affecting the maxillae. They observed the disorder in a mother, 2 of her daughters, and a son. Articles from Dentomaxillofacial Radiology are provided here courtesy of British Institute of Radiology.

Articles from Medicine are provided here courtesy of Wolters Kluwer Health. E Technetium scintigraphy showed increased tracer uptaker in the chin area. Incomplete excision or shave-off contouring is not advised because it may cause a possible aggravation or reactivation of rapid FGC growth.

Surgical removal of the affected bone is needed, and has to be followed by reconstruction. Among all the reports available, Rossbach et al 3 was the first to postulate the giigantiform of a brittle bone disorder with FGC. All these fractures, which occurred in diaphyseal locations, were categorized to a minor-trauma or spontaneous causes owing to poor evidence of outside forces.

From This Paper Figures, tables, and topics from this paper. C Lateral view of FGC. Familial gigantiform cementoma with brittle bone disease, pathologic fractures, and osteosarcoma: Plast Reconstr Surg ;